Anti-SUOX Antibody (CAB0733)
- SKU:
- CAB0733
- Product type:
- Antibody
- Antibody Type:
- Monoclonal Antibody
- Reactivity:
- Rat
- Host Species:
- Rabbit
- Isotype:
- IgG
- Synonyms:
- SUOX
- Synonyms:
- sulfite oxidase
Frequently bought together:
Description
| I抗体名: | SUOX Rabbit mAb |
| 抗体コード: | CAB0733 |
| サイズ: | 20uL, 50uL, 100uL |
| 同義語: | SUOX, sulfite oxidase |
| 申し込み: | WB |
| 反応性: | Rat |
| 宿主種: | Rabbit |
| 免疫原: | A synthesized peptide derived from human SUOX. |
| 申し込み: | WB |
| 推奨される希釈: | WB 1:500 - 1:2000 |
| 反応性: | Rat |
| ポジティブサンプル: | Rat kidney |
| 免疫原: | A synthesized peptide derived from human SUOX. |
| 精製方法: | Affinity purification |
| 保管所: | Store at -20°C. Avoid freeze / thaw cycles. Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
| アイソタイプ: | IgG |
| 順序: | Email for sequence |
| 遺伝子ID: | 6821 |
| Uniprot: | P51687 |
| セルラーロケーション: | Mitochondrion intermembrane space |
| 計算された分子量: | 60kDa |
| 観察された分子量: | 60KDa |
| UniProt Protein Function: | SUOX: Defects in SUOX are the cause of isolated sulfite oxidase deficiency (ISOD); also known as sulfocysteinuria. ISOD is characterized by neurological abnormalities including multicystic leukoencephalopathy with brain atrophy. Patients often suffer from seizures. Often leads to death at an early age. |
| UniProt Protein Details: | Protein type:Mitochondrial; Energy Metabolism - sulfur; Oxidoreductase; EC 1.8.3.1 Chromosomal Location of Human Ortholog: 12q13.2 Cellular Component: mitochondrial matrix; mitochondrial intermembrane space Molecular Function:molybdopterin cofactor binding; electron carrier activity; molybdenum ion binding; heme binding; sulfite oxidase activity Biological Process: sulfur amino acid metabolic process; sulfur amino acid catabolic process Disease: Sulfocysteinuria |
| NCBI Summary: | Sulfite oxidase is a homodimeric protein localized to the intermembrane space of mitochondria. Each subunit contains a heme domain and a molybdopterin-binding domain. The enzyme catalyzes the oxidation of sulfite to sulfate, the final reaction in the oxidative degradation of the sulfur amino acids cysteine and methionine. Sulfite oxidase deficiency results in neurological abnormalities which are often fatal at an early age. Alternative splicing results in multiple transcript variants encoding identical proteins. [provided by RefSeq, Jul 2008] |
| UniProt Code: | P51687 |
| NCBI GenInfo Identifier: | 152031695 |
| NCBI Gene ID: | 6821 |
| NCBI Accession: | P51687.2 |
| UniProt Related Accession: | P51687 |
| Molecular Weight: | 545 |
| NCBI Full Name: | Sulfite oxidase, mitochondrial |
| NCBI Synonym Full Names: | sulfite oxidase |
| NCBI Official Symbol: | SUOX |
| NCBI Protein Information: | sulfite oxidase, mitochondrial |
| UniProt Protein Name: | Sulfite oxidase, mitochondrial |
| Protein Family: | Sulfite oxidase |
| UniProt Gene Name: | SUOX |
| UniProt Entry Name: | SUOX_HUMAN |
Related Products
Anti-Anti-TrkB Antibody (CAB19832)
€0.00
概要抗体名:Anti-TrkB Rabbit mAb抗体コード:CAB19832サイズ:20uL, 50uL, 100uL同義語:GP145-TrkB/GP95-TrkB, Tkrb, trk-B, trkB申し込み:
Human SUOX ELISA Kit (HUFI06253)
€0.00
概要商品名:Human SUOX ELISA Kit 製品コード:HUFI06253サイズ:96Tエイリアス:SUOX ELISA Kit検出方法:Sandwich ELISA, Double Antibody
Human anti-EPO antibody(anti-Erythropoietin antibody) ELISA Kit
€0.00
system_update_altデータシートsystem_update_alt安全性データシート